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CASE REPORT
Leiomyosarcoma of the right renal vein with tumour thrombus extending to the right atrium – Case Report and literature review
1
Department of Urology and Urologic Oncology, Medical University, Lublin, Poland
2
Department of Clinical Oncology and Chemotherapy, Medical University, Lublin, Poland
Corresponding author
Michał Godzisz
Department of Urology and Urologic Oncology, Medical University of Lublin, Jaczewskiego 8, 20-954, Lublin, Poland
Department of Urology and Urologic Oncology, Medical University of Lublin, Jaczewskiego 8, 20-954, Lublin, Poland
KEYWORDS
TOPICS
ABSTRACT
Leiomyosarcoma (LMS) is a mesenchymal neoplasm accounting for 20% of all soft tissue sarcomas (STS), with a particularly
rare localization in the muscular layer of the venous vessels. The case report presents a patient with non-metastatic LMS of
the right renal vein, spreading intraluminally, and reaching the right atrium of the heart, supplemented with a review of the
state of knowledge. The patient underwent radical treatment, including radical nephrectomy with en bloc thrombectomy
under extracorporeal circulation without circulatory arrest and deep hypothermia. Histopathological examination diagnosed
LMS and negative surgical margins. A computed tomography (CT) scan performed on the 45th postoperative day detected
no early recurrence or metastatic features. The world literature describes 78 cases of renal vein (RV) LMS. Surgical treatment
has the greatest overall survival (OS) impact. Adjuvant systemic treatment and radiotherapy do not improve OS outcomes,
having only palliative significance.
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| eISSN: | 1898-2263 |
| ISSN: | 1232-1966 |
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