Granular cell tumour (GCT) or Abrikossoff tumour, is a rare submucosal neoplasm orginating from Schwann cells, and accounts for 0.03% of all submucusal tumours. Only 8% of GCTs occur in the gastrointestinal tract, mostly in the esophagus. Diagnosis of granular cell tumour is exceptionally rare. The case is presented of a 72-year-old female patient who underwent polypectomy of a colon polyp which, in the histopathology report, appeared to be a granular cell tumour. The possibility of granular cell tumour diagnosis which is extremly rare, is discussed. However, 2% of these tumours are malignant. It is very important to establish the diagnosis as early as possible. The patient was admitted to the Gastroenterology Outpatient Clinic due to a hepatic vascular lesion. She did not present any symptoms of granular cell tumour. A complete resection of the granular cell tumour fortunately confirmed it to be benign.